Bottom line: Inherited condition associated with severe hypertension and hypokalemia.
Concise answer: Metabolic disorders. In: Brenner and Rector’s The Kidney, 8th ed.
Detailed answer: Gennari FJ, et al An unusual case of metabolic alkalosis: a window into the pathophysiology and diagnosis of this common acid-base disturbance. Am J Kidney Dis. 2010 Jun;55(6):1130-5.
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